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科研文章

Case Report: Report of Two Cases of Interstitial Lung Disease Caused by Novel Compound Heterozygous Variants in the ABCA3 Gene

Chen F, Xie Z, Zhang VW, Chen C, Fan H, Zhang D, Jiang W, Wang C, Wu P.Front Genet. 2022 Apr 6;13:875015.35464853

Case Report: Be Aware of "New" Features of Niemann-Pick Disease: Insights From Two Pediatric Cases

Chen F, Guo S, Li X, Liu S, Wang L, Zhang VW, Xu H, Huang Z, Ying Y, Shu S. Front Genet. 2022 Mar 11;13:845246. 35360843

Expanding the mutational spectrum of Rahman syndrome: A rare disorder with severe intellectual disability and particular facial features in two Chinese patients

Zhao J, Lyu G, Ding C, Wang X, Li J, Zhang W, Yang X, Zhang VW. Mol Genet Genomic Med. 2022 Feb 14:e1825. 35156329

Identification and Functional Characterization of a Novel Nonsense Variant in ARR3 in a Southern Chinese Family With High Myopia

Yuan D, Yan T, Luo S, Huang J, Tan J, Zhang J, Zhang VW, Lan Y, Hu T, Guo J, Huang M, Zeng D. Front Genet. 2021 Dec 13;12:765503.

Missense mutation in DYNC1H1 gene caused psychomotor developmental delay and muscle weakness: A case report

Ding FJ, Lyu GZ, Zhang VW, Jin H. World J Clin Cases. 2021 Oct 26;9(30):9302-9309. 34786417

Kv3.1 channelopathy: a novel loss-of-function variant and the mechanistic basis of its clinical phenotypes

Li X, Zheng Y, Li S, Nair U, Sun C, Zhao C, Lu J, Zhang VW, Maljevic S, Petrou S, Lin J. Ann Transl Med. 2021 Sep;9(18):1397. 34733949

Mesenchymal stem cells from different sources show distinct therapeutic effects in hyperoxia-induced bronchopulmonary dysplasia in rats

Xie Y, Chen F, Jia L, Chen R, Zhang VW, Zhong X, Wang D. J Cell Mol Med. 2021 Sep;25(17):8558-8566. 34322990

Exome-based preconception carrier testing for consanguineous couples in China

He Y, Xie RG, Lou JW, Li YW, Wang CL, Zhang VW, Li DZ. Prenat Diagn. 2021 Oct;41(11):1425-1429.34486758

Clinical Utility of Rapid Exome Sequencing Combined With Mitochondrial DNA Sequencing in Critically Ill Pediatric Patients With Suspected Genetic Disorders

Ouyang X, Zhang Y, Zhang L, Luo J, Zhang T, Hu H, Liu L, Zhong L, Zeng S, Xu P, Bai Z, Wong LJ, Wang J, Wang C, Wang B, Zhang VW. Front Genet. 2021 Aug 19;12:725259. 34490048

Parental mosaicism in de novo neurodevelopmental diseases

Shu L, Zhang Q, Tian Q, Yang S, Zhang VW, Peng X, Mao X, Yang L, Du J, Wang H. Am J Med Genet A. 2021 Jul;185(7):2119-2125. 33851778

Novel Mutations in the GTPBP3 Gene for Mitochondrial Disease and Characteristics of Related Phenotypic Spectrum: The First Three Cases From China

Yan HM, Liu ZM, Cao B, Zhang VW, He YD, Jia ZJ, Xi H, Liu J, Fang F, Wang H. Front Genet. 2021 Jul 1;12:611226. 34276756

Case Report: Two Chinese Infants of Sengers Syndrome Caused by Mutations in AGK Gene

Wang B, Du Z, Shan G, Yan C, Zhang VW, Li Z. Front Pediatr. 2021 Jun 7;9:639687. 34164355

Report of a case with ferredoxin reductase (FDXR) gene variants in a Chinese boy exhibiting hearing loss, visual impairment, and motor retardation

Yang C, Zhang Y, Li J, Song Z, Yi Z, Li F, Xue J, Zhang W, Wang C. Int J Dev Neurosci. 2021 Jun;81(4):364-369.33742450

Whole exome sequencing identifies a novel homozygous MECR mutation in a Chinese patient with childhood-onset dystonia and basal ganglia abnormalities, without optic atrophy

Liu Z, Shimura M, Zhang L, Zhang W, Wang J, Ogawa-Tominaga M, Wang J, Wang X, Lv J, Shi W, Zhang VW, Murayama K, Fang F. Mitochondrion. 2021 Mar;57:222-229.33401012

Autosomal dominant tubulointerstitial kidney disease genotype and phenotype correlation in a Chinese cohort

Gong K, Xia M, Wang Y, Wang N, Liu Y, Zhang VW, Cheng H, Chen Y. Sci Rep. 2021 Feb 11;11(1):3615. 33574344

Prenatal phenotypic discordance in monozygotic twins due to a postzygotic TSC2 variant

Zhen L, Guo J, Jiang F, Xu LL, Zhang VW, Li DZ.Prenat Diagn. 2021 Jan;41(2):207-209. 33074564

Identification of thalassemia gene cluster deletion by long-read whole-genome sequencing (LR-WGS)

Jiang F, Lyu GZ, Zhang VW, Li DZ.Int J Lab Hematol. 2021 Aug;43(4):859-865.33400392

Novel TARDBP missense mutation caused familial amyotrophic lateral sclerosis with frontotemporal dementia and parkinsonism

Chen S, Zhou RL, Zhang W, Che CH, Feng SY, Huang HP, Liu CY, Zou ZY. Neurobiol Aging. 2021 Nov;107:168-173.34175147

Simultaneous Detection of CNVs and SNVs Improves the Diagnostic Yield of Fetuses with Ultrasound anomalies and Normal Karyotypes

Qi Q, Jiang Y, Zhou X, Meng H, Hao N, Chang J, Bai J, Wang C, Wang M, Guo J, Ouyang Y, Xu Z, Xiao M, Zhang VW, Liu J.Genes (Basel). 2020 Nov 25;11(12):1397.33255631

The Study of Genetic Susceptibility and Mitochondrial Dysfunction in Mesial Temporal Lobe Epilepsy

Yang H, Yin F, Gan S, Pan Z, Xiao T, Kessi M, Yang Z, Zhang VW, Wu L.Mol Neurobiol. 2020 Sep;57(9):3920-3930. 32632602

B-lymphocyte deficiency and recurrent respiratory infections in a 6-month-old female infant with mosaic monosomy 7

Mai K, Chen X, Wang C, Wu S, Yang L, Huang Z, Zhang G, Zhang VW, Wang J, Chen D. Immunobiology. 2020 Sep;225(5):152005. 32962823

Novel Biallelic Variants in COL7A1 Cause Recessive Dystrophic Epidermolysis Bullosa

Yang N, Ma Y, Yao H, Chang Q, Zhang V, Liang Z, Cai X.Mol Genet Genomic Med. 2020 Aug;8(8):e1347.32537942

Clinical and laboratory interpretation of mitochondrial mRNA variants

Wong LC, Chen T, Schmitt ES, Wang J, Tang S, Landsverk M, Li F, Zhang S, Wang Y, Zhang VW, Craigen WJ.Hum Mutat. 2020 Oct;41(10):1783-1796.32652755

Interpretation of Mitochondrial tRNA Variants

Wong LC, Chen T, Wang J, Tang S, Schmitt ES, Landsverk M, Li F, Wang Y, Zhang S, Zhang VW, Craigen WJ.Genet Med. 2020 May;22(5):917-926.31965079

L1CAM Mutations in Three Fetuses Diagnosed by Medical Exome Sequencing

Li YT, Chen JS, Jian W, He YD, Li N, Xie YN, Wang J, Zhang VW, Huang WR, Jiang FM, Ye XQ, Chen DJ, Chen M.Taiwan J Obstet Gynecol. 2020 May;59(3):451-455.32416898

Clinical Application of Medical Exome Sequencing for Prenatal Diagnosis of Fetal Structural Anomalies

Chen M, Chen J, Wang C, Chen F, Xie Y, Li Y, Li N, Wang J, Zhang VW, Chen D.Front Neurol.Eur J Obstet Gynecol Reprod Biol. 2020 Aug;251:119-124.32502767

Identification and Clinical Analysis of the First Nonsense Mutation in the PSEN1 Gene in a Family With Acute Encephalopathy and Retinitis Pigmentosa

You C, Zeng W, Deng L, Lei Z, Gao X, Zhang VW, Wang Y.Front Neurol. 2020 May 5;11:319.32431660

Profiling of Mitochondrial Genomes in SCA3/MJD Patients From Mainland China

Yuan H, Yang H, Peng L, Peng Y, Chen Z, Wan L, Wang C, Shi Y, Zhang VW, Tang B, Qiu R, Jiang H.Gene. 2020 May 15;738:144487. 32087274

Rapid Prenatal Diagnosis of Skeletal Dysplasia Using Medical Trio Exome Sequencing: Benefit for Prenatal Counseling and Pregnancy Management

Han J, Yang YD, He Y, Liu WJ, Zhen L, Pan M, Yang X, Zhang VW, Liao C, Li DZ.Prenat Diagn. 2020 Apr;40(5):577-584. 31994750

Genetic Examination for Fetuses With Increased Fetal Nuchal Translucency by Genomic Technology

Shuya Xue, Huanchen Yan, Jingsi Chen, Nan Li, Jiayan Wang, Yu Liu, Huimin Zhang, Shaoying Li, Wei Zhang, Dunjin Chen, Min Chen.Cytogenet Genome Res. 2020 Feb;160(2):57-62.32036363

Novel SPEG variant cause centronuclear myopathy in China

Tang J, Ma W, Chen Y, Jiang R, Zeng Q, Tan J, Jiang H, Li Q, Zhang VW, Wang J, Tang H, Luo L.J Clin Lab Anal. 2020 Feb;34(2):e23054.31625632

Mutations in both SAMD9 and SLC19A2 genes caused complex phenotypes characterized by recurrent infection, dysphagia and profound deafness - a case report for dual diagnosis

Zhang Y, Zhang Y, Zhang VW, Zhang C, Ding H, Yin A.BMC Pediatr. 2019 Oct 21;19(1):364.31638924

The nuclear background influences the penetrance of the near-homoplasmic m.1630 A > G MELAS variant in a symptomatic proband and asymptomatic mother

Uittenbogaard M, Wang H, Zhang VW, Wong LJ, Brantner CA, Gropman A, Chiaramello A.Mol Genet Metab. 2019 Apr;126(4):429-438. 30709774

Loss-of-function mutations in Lysyl-tRNA synthetase cause various leukoencephalopathy phenotypes

Chong Sun, Jie Song, Yanjun Jiang, Chongbo Zhao, Jiahong Lu, Yuxin Li, Yin Wang, Mingshi Gao, Jianying Xi, Sushan Luo, Meixia Li, Kevin Donaldson, Stephanie N. Oprescu, Thomas P. Slavin, Sansan Lee, Pilar L. Magoulas, Andrea M. Lewis, Lisa Emrick, Seema R. Lalani, Zhiyv Niu, Megan L. Landsverk, Magdalena Walkiewicz, Richard E. Person, Hui Mei, Jill A. Rosenfeld, Yaping Yang, Anthony Antonellis, Ya-Ming Hou, Jie Lin, and Victor W. Zhang.Neurol Genet. 2019 Apr 18;5(2):e565.31192300

De Novo Mutated TUBB2B Associated Pachygyria Diagnosed by Medical Exome Sequencing and Long-Range PCR

Wang H, Li S, Li S, Jiang N, Guo J, Zhang W, Zhong M, Xie J.Fetal Pediatr Pathol. 2019 Feb;38(1):63-71.30585108

Identification of a novel DNMT1 mutation in a Chinese patient with hereditary sensory and autonomic neuropathy type IE

Zheng W, Yan Z, He R, Huang Y, Lin A, Huang W, Su Y, Li S, Zhang VW, Xie H.BMC Neurol. 2018 Oct 20;18(1):174.30342480


De Novo Mutations of CCNK Cause a Syndromic Neurodevelopmental Disorder with Distinctive Facial Dysmorphism

Fan Y, Yin W, Hu B, Kline AD, Zhang VW, Liang D, Sun Y, Wang L, Tang S, Powis Z, Li L, Yan H, Shi Z, Yang X, Chen Y, Wang J, Jiang Y, Tan H, Gu X, Wu L, Yu Y. Am J Hum Genet. 2018 Sep 6;103(3):448-455.30122539

Giant bilateral adrenal myelolipomas in two Chinese families with congenital adrenal hyperplasia

Liu Q, Wang LA, Su J, Tong D, Lan W, Wang L, Liu G, Zhang J, Zhang VW, Zhang D, Chen R, Zhu Q, Jiang J. Endocr Connect. 2018 Sep 1.30352423

The clinical spectrum and genetic variability of limb-girdle muscular dystrophy in a cohort of Chinese patients

Wang L, Zhang VW, Li S, Li H, Sun Y, Li J, Zhu Y, He R, Lin J, Zhang C. Orphanet J Rare Dis. 2018 Aug 14;13(1):133.30107846

A Rare Hb H Hydrops Fetalis Syndrome Caused by the - -SEA Deletion in Combination with the Rare Hb Hirosaki Mutation in a Chinese Patient

Li Q, Li Y, Zhong M, Zhang VW, Jin W, Li S, Li L.Hemoglobin. 2018 Jul;42(4):278-280. 30486690

Novel mutations in HINT1 gene cause the autosomal recessive axonal neuropathy with neuromyotonia

Wang Z, Lin J, Qiao K, Cai S, Zhang VW, Zhao C, Lu J. Eur J Med Genet. 2018 Jul 11. pii: S1769-7212(18)30266-0.30006059

The next generation of population-based spinal muscular atrophy carrier screening: comprehensive pan-ethnic SMN1 copy-number and sequence variant analysis by massively parallel sequencing

Feng Y, Ge X, Meng L, Scull J, Li J, Tian X, Zhang T, Jin W, Cheng H, Wang X, Tokita M, Liu P, Mei H, Wang Y, Li F, Schmitt ES, Zhang WV, Muzny D, Wen S, Chen Z, Yang Y, Beaudet AL, Liu X, Eng CM, Xia F, Wong LJ, Zhang J. Genet Med. 2017 Aug;19(8):936-944.28125085

Two novel mutations in the PPIB gene cause a rare pedigree of osteogenesis imperfecta type IX

Jiang Y, Pan J, Guo D, Zhang W, Xie J, Fang Z, Guo C, Fang Q, Jiang W, Guo Y. Clin Chim Acta. 2017 Jun;469:111-118.28242392

Genetic evidence of 'genuine' empty follicle syndrome: a novel effective mutation in the LHCGR gene and review of the literature

Yuan P, He Z, Zheng L, Wang W, Li Y, Zhao H, Zhang VW, Zhang Q, Yang D. Hum Reprod. 2017 Apr 1;32(4):944-953.28175319